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Inborn hemangioma

Inborn hemangioma — a benign vascular tumor.

Epidemiology

Arises at early children's age, a thicket at girls, in 75 — 90% there is an involution to 7-year age.

Classification

Capillary hemangioma.
Cavernous hemangioma.

Etiology and pathogeny

Proliferation of endotheliocytes with formation of capillaries is the cornerstone of development of a tumor that is confirmed positive reactions with E-selectin. Skin defeats can often be markers of the hidden angiomas of internals.

Clinical signs and symptoms

The most frequent localization of an inborn hemangioma — the head and a neck.
• The capillary hemangioma is characterized by cyanotic-red or crimson spots, sometimes the speakers over a skin surface who are turning pale when pressing. Option is the star-shaped angioma in the form of a dot red spot with the capillary vessels departing from it. Sometimes the capillary hemangioma is combined with thrombocytopenia and purpura (Kazabakh's syndrome — Merritt).
• The cavernous hemangioma represents a limited tumor of color of normal skin — at a deep arrangement — or red color with a cyanotic shade — at exophytic nature of education. The new growth surface smooth, but can be lobular with a hyperkeratosis or verrukozny. Spontaneous regressing of a tumor till the puberty period is observed, however the current can be and progressing with destruction of adjacent fabrics. The cavernous hemangioma can be combined with a capillary hemangioma. Unilateral localization of this tumor is in certain cases described. Besides, the combination to thrombocytopenia (Kazabakh's syndrome — Merritt) and a combination of multiple cavernous hemangiomas to a dyschondroplasia as a result of defect of ossification, fragility of bones, their deformation and formation of osteochondromas which can turn into a chondrosarcoma (a syndrome of Mafuchchi) meets.

The diagnosis and the recommended clinical trials

For determination of depth and volume of cavernous angiomas the angiography, a magnetic and resonant tomography are shown.
The node consists of various number of capillaries, sometimes closely adjacent to each other in this connection the tumor gets a solid structure. In an initial stage of growth the tumor consists from tyazhy the proliferating endotheliocytes in which in places it is possible to find very narrow gleams. In the mature centers gleams of capillaries wider, and the endothelium covering them is flattened. Further in a regressing stage in a stroma of a tumor fibrous fabric which squeezes and substitutes neogenic capillaries expands. It leads to wrinkling and a total disappearance of the centers of defeat. Sometimes vessels of other type, mostly venous occur among capillaries. In such cases the similar tumor is called the mixed hemangioma.
In a cavernous hemangioma distinguish 2 versions — with an arterial and venous differentiation of vascular walls. The numerous large vessels with an expanded gleam covered by the thinned endothelium are located deeply in a derma and hypodermic fatty tissue, walls of vessels thick with symptoms of fibrosis of an extima.

General principles of treatment of an inborn hemangioma

Limited defeats: a cryolysis, electrocoagulation, surgical excision, laser destruction (the pulse laser with the wavelength of 532 nanometers), an intra focal sklerozirovaniye, obkalyvany GKS, a roentgenotherapy beams Beeches.

Forecast

Favorable.
 
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