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Angiopathies - Practical hematology of children's age

Table of contents
Practical hematology of children's age
Embryonal hemopoiesis
Morfofunktsionalny characteristic of cells of marrow and peripheral blood
Marrow parenchyma cells
Peripheral blood of children of different age
The system of a hemostasis is normal
Etiology and pathogeny of leukoses
Acute leukoses
Acute leukoses - a preleukosis
Possibilities of a predictive assessment of a course of an acute lymphoblastoid leukosis at children
General principles of treatment of an acute leukosis
Chemotherapeutic drugs
Treatment of an acute lymphoblastoid leukosis
Treatment of myeloid forms of an acute leukosis
Infectious complications and symptomatic therapy of an acute leukosis
Consolidation and maintenance therapy of an acute leukosis
Immunotherapy
Remission and recurrence of an acute leukosis
Inborn leukosis
Neuroleukosis
Myelosis
Lymphogranulomatosis
Gematosarkoma
Macrofollicular lymphoma
Angioimmunoblastny lymphadenopathy
Leukemoid tests
Infectious lymphocytosis
Infectious mononucleosis
Leukemoid tests of different types
Dysfunctions of granulocytes
Leukopenias
Histiocytoses
Histiocytoses - an eosinophilic granuloma
Malignant histiocytosis
Family erythrophagocytal histiocytosis
Accumulation diseases
Nimann's illness — Peak
Angiopathies
Hemorrhagic vasculitis (Shenleyn's illness — Genokh)
Mayokki's purpura
Ataxy teleangiectasia
Entsefalotrigeminalny angiomatosis
Kortiko-meningealny diffusion angiomatosis
Cerebroretinal angiomatosis
Hypertrophic gemangiektaziya
Multiple and huge hemangiomas
Elastic fibrodisplaziya
Coagulopathies
Hereditary coagulopathies
Hemophilia And
Clinic of hemophilia
Treatment of hemophilia
Angiohemophilia
Cristmas disease (Kristmas's illness)
Hereditary deficit of factors of XI, XII, XIII and I
Dysfibrinogenemias
Hereditary deficit of factors of VII, X, V and II
Deficit K-vitaminozavisimykh of factors of coagulation
Syndrome of the disseminated intravascular coagulation
Clinic and diagnosis of the IDCS
Treatment of the IDCS
Thrombocytopenia
Idiopathic Werlhof's disease
Clinic and diagnosis of an idiopathic Werlhof's disease
Treatment of an idiopathic Werlhof's disease
Isoimmune Werlhof's disease
Transimmune Werlhof's disease of newborns
Trombogemolitichesky Werlhof's disease (syndrome Moshkovich)
Hereditary Werlhof's diseases
Trobotsitopatiya
Anemias
The anemias connected with blood loss
Chronic posthemorrhagic anemia
Iron deficiency anemias
Clinic and diagnosis of an iron deficiency anemia
Treatment of iron deficiency anemias
Sideroakhrestichesky, sideroblastny anemias
Megaloblastny anemias
Foliyevodefitsitny anemia
Hereditary forms of megaloblastny anemias
Hereditary dizeritropoetichesky anemias
The anemias connected with oppression of proliferation of cells of marrow
Hereditary hypoplastic anemias
Hemolitic anemias
Hemolitic anemias - an ovalocytosis, a hereditary stomatocytosis
Acanthocytosis, piknotsitoz
The hereditary hemolitic anemias connected with disturbance of activity of enzymes of erythrocytes
The hereditary hemolitic anemias connected with disturbance of structure or synthesis of hemoglobin
The acquired immune hemolitic anemias
Isoimmune hemolitic anemias
Treatment of a hemolitic illness of newborns
Autoimmune hemolitic anemias
List of references

Chapter VII
HEMORRHAGIC DIATHESIS
ANGIOPATHIES
Hemorrhagic angiopathies are a group of diseases which cornerstone defeat of a vascular link of system of a hemostasis is that causes the raised bleeding. The etiology and a pathogeny of hemorrhagic angiopathies are various, they can be as a separate nosological form, and to represent a hemorrhagic syndrome of a basic disease. Classification and the nomenclature of hemorrhagic syndromes of a vascular origin remain a controversial issue so far. However the group of angiopathies on etiological and pathogenetic signs has great practical value as arms the doctor with understanding of essence of hemorrhagic manifestations and the corresponding approaches to therapy.
Allocate several main groups of hemorrhagic angiopathies (V. A. Germanov, 1979).

  1. Immunocomplex hemorrhagic angiopathies which cornerstone damage of a vascular wall by a cell-bound immune complex antigen — an antibody is. The hemorrhagic vasculitis as an independent nosological form belongs to this group of diseases. Immunocomplex hemorrhagic angiopathies as a syndrome are observed at many immunopathological processes, in particular collagenoses, infektsionnoallergichesky diseases, etc.
  2. Infectious hemorrhagic angiopathies are complications of heavy infectious process. They are observed at a meningokokktsemiya, viral diseases (measles, a rubella, flu), viral hemorrhagic fevers, a hay fever, sapropyra, especially dangerous infections (natural smallpox, plague).
  3. Metaplastic hemorrhagic angiopathies which cornerstone tumoral defeat of a vascular wall is. They are observed at different malignant oncological diseases. In many cases the hemorrhagic syndrome is combined on the genesis when there is a defeat not only vessels, but also a platelet link of system of a hemostasis.
  4. Dysplastic hemorrhagic angiopathies are the hereditary or inborn diseases caused by maldevelopment of connecting fabric. They represent the hemangiomas having the different sizes and localization. Formation of macrohemangiomas, and also their localization in vitals constitutes serious danger and a possibility of a lethal outcome. Feature of hemorrhagic angiopathies is the raised bleeding from defective places and development of posthemorrhagic anemia, sometimes heavy degree. Bleedings arise spontaneously at inadequate influence. Treat group of dysplastic hemorrhagic angiopathies: an illness of Randyu — Oslera, Kazabakh's syndromes — Merritt, Elers — Danlosa, Louis Bar, Gippel — Lindau, etc.
  5. Dystrophic hemorrhagic angiopathies at which functional disturbances of a vascular wall are caused by disturbance of food of cells and fabrics — cellular dystrophy. They arise at hypo - and avitaminosis (deficit of ascorbic acid and vitamin P), endocrinopathies, beam impact on an organism, aging of fabrics and vessels. Dystrophic hemorrhagic angiopathies are the syndrome of a basic disease complicating its current. Dystrophic changes of vessels are characteristic of exogenous and endogenous insufficiency of ascorbic acid, the shown bleeding of gums and hemorrhages on skin and in gastrocnemius muscles.
  6. Neuropathic hemorrhagic angiopathies which description belongs to Middle Ages times. In the history of religion there were certificates on persons who in religious ecstasy cried bloody tears. In modern literature a number of hemorrhagic manifestations of neurogenic character is described; as a rule, they are marked out at persons with the changed psychoemotional status though can be observed at almost healthy people in the mental relation during the periods of the raised emotional loading.

It is noted that much not true neuropathic hemorrhagic angiopathies, and imitation, simulation of a hemorrhagic syndrome meet more often (3. S. Barkagan, 1980). Such situations occur at children considerably less than at adults.



 
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