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The Indian juvenile cirrhosis - Diseases of digestive organs at children

Table of contents
Diseases of digestive organs at children
Oral cavity
Diseases of teeth
Malformations of the sky and soft tissues of an oral cavity
Diseases of a mucous membrane of an oral cavity and gums
Diseases of lips and language
Sialadens
Digestive tract
Basic reasons of gastrointestinal frustration
Gullet
Atresia and esophageal and tracheal fistula
Guttural and tracheal and esophageal crevice, inborn stenosis of a gullet
Other diseases of a gullet
Stomach and intestines
Peptic ulcer
Inborn hypertrophic pyloric stenosis
Inborn impassability of intestines
Inborn impassability of a duodenum
Disturbances of turn of intestines
Inborn impassability of a small bowel
Inborn megacolon
Diverticulums and duplikatura
The acquired impassability of intestines
Intestines invagination
Foreign bodys of a stomach and intestines
Motive frustration. stomach and intestines
Anomalies of a structure of anorectal area
Infectious diseases of intestines
Nonspecific ulcer colitis
Illness Krone
Necrotic coloenteritis of newborns
The coloenteritis connected with treatment by antibiotics
Gastrointestinal symptoms of anaphylactoid purpura, gemolitiko-uraemic syndrome
Intolerance of food proteins
Eosinophilic gastroenteritis
Absorption disturbance syndromes
Malabsorption
Immunodeficiency and intestines
Syndrome of "a congestive loop"
Syndrome of a short small bowel
Gee's disease
Sprue after acute enteritis
Tropical to a spr
Whipple's illness, intestines lymphangiectasia, Uolmap's illness, idiopathic diffusion defeat of mucous
Enzymopathies and disturbances of mechanisms of transport of nutrients
Irritable colon
Acute appendicitis
Diseases of an anus, direct and large intestine
Tumors of a digestive tract at children
Hernias of a digestive tract at children
Exocrine part of a pancreas
Pancreatitis
Embryonic development of structure and function of a liver
Diagnosis of diseases of a liver
Cholestatic states at babies
Parenchymatous jaundices at children of chest age
Disturbances of a metabolism of a liver and zhelchevydelitelny system
Anomalies of a structure of bilious ways
Cysts of bilious channels
Cholestasia and diseases of a liver connected with completely parenteral food
Medicinal damage of a liver
Ray's syndrome
Chronic hepatitis
Wilson's illness — Konovalova
Indian juvenile cirrhosis
Damages of a liver at chronic colitis
Cirrhosis and chronic liver failure
Portal hypertensia and varicosity of a gullet
Fatty infiltration of a liver
Cholecystitis
Peritoneum diseases
Peritonitis
Peritoneum hernias

The Indian juvenile cirrhosis - it the family disease of children of preschool age is widespread on the Indian subcontinent, but meets also on the Middle East, in the Western Africa and Central America. The peak of incidence is the share of age 1 — 5 flying, boys and girls are ill equally often. The mode of inheritance is not established yet; it is possible that the pathogeny is defined by action of the external factors accumulating on genetic predisposition.
Clinical and datas of laboratory. The beginning is usually gradual, but also rapid development of process is possible. The first sign — an asymptomatic hepatomegalia, then there are symptoms of an acute viral hepatitis, such as fever, anorexia, decoloured by kcal, dark urine, jaundice. In one cases the illness quickly passes into cirrhosis, in others — spontaneously stops at any stage. Standard biochemical indicators of functions of a liver are changed, however the only sign specific to this illness — sharp increase of level of serumal immunoglobulins.
Patomorfologiya. In the serial bioptata taken in process of a course of a disease transition from the acute inflammatory process reminding a viral hepatitis to the step necrosis and development of cicatricial fabric characteristic of chronic active hepatitis comes to light. At quickly progressing (malignant) current in a pathomorphologic picture the necrosis, a cellular degeneration and wrinkling of segments prevail. In the hepatocytes surrounded with inflammatory cells Mallori's little bodies are visible. The centers of a necrosis are substituted with cicatricial fabric therefore mikronodulyarny cirrhosis develops. Coloring by orcein reveals considerable deposits of copper, mainly in lysosomes.
Treatment. Specific therapy does not exist. Corticosteroids can as at chronic active hepatitis to lead to long remission.
Forecast. Most of children perish within one year. At survivors slow cirrhosis forms.



 
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